Gorlin-Goltz Syndrome: a clinic case report
DOI:
https://doi.org/10.5281/zenodo.14876615Keywords:
basal cell nevus syndrome, odontogenic cysts, neoplasmAbstract
Gorlin-Goltz Syndrome is a clinic hereditary disorder related to a number of manifestations that commonly presents odontogenic keratocytes. The clinical case of a sixteen-year-old male patient, diagnosed with Gorlin-Goltz Syndrome, was presented. A radiographic method was performed and it revealed the presence of various cysts in both maxillaries that were associated to retained teeth; therefore, he was referred to the Maxillofacial Surgery Service of the Pediatric Hospital. A surgery of the lesion that occupied part of the left mandible body and upper branch was done and a biopsy was taken. Gorlin-Goltz Syndrome is a genetic condition of low incidence; the group of its main manifestations increases data for the analysis of differential diagnosis to be considered by the dentist and pediatric maxillofacial surgeon, and enriches the efforts for scientific researches.
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